Costameric distribution of beta-dystroglycan (43 kDa dystrophin-associated glycoprotein) in normal and dystrophin-deficient human skeletal muscle.
نویسندگان
چکیده
23 Hagiwara, Y. and Ozawa, E. (1994) Eur. J. Biochem. 220,283-292 24 Suzuki, A., Yoshida, M. and Ozawa, E. (1995) J. Cell Biol. 128, 373-381 Tuffery, S., Lenk, U., Roberts, R. G., Coubes, C., Demaille, J. and Claustres, M. (1995) Hum. Mutat. 6, 126-135 Merlie, J. P. (1995) Neuron 15, 115-126 Scotland, P. B., Colledge, M., Melinkova, I., Dai, 2. and Froehner, S. C. (1993) J. Cell Biol. 123, 7 19-728 50 I
منابع مشابه
The Dystrophin Complex Forms a Mechanically Strong Link between the Sarcolemma and Costameric Actin
The absence of dystrophin complex leads to disorganization of the force-transmitting costameric cytoskeleton and disruption of sarcolemmal membrane integrity in skeletal muscle. However, it has not been determined whether the dystrophin complex can form a mechanically strong bond with any costameric protein. We performed confocal immunofluorescence analysis of isolated sarcolemma that were mech...
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عنوان ژورنال:
- Biochemical Society transactions
دوره 24 2 شماره
صفحات -
تاریخ انتشار 1996